Cutaneous types of mastocytosis in paediatry. Case report of maculopapular cutaneous mastocytosis in an infant

Olga B. Tamrazova , Evgeniya A. Glukhova

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Abstract

Mastocytosis is a heterogeneous group of neoplasms characterized by increased mast cells proliferation and accumulation in various organs and tissues. The paper introduces the newest mastocytosis classification and diagnosis principles. Each type of cutaneous mastocytosis is discussed separately, with the recommendations for the affected patients’ management. The paper reports the typical mastocytosis manifestations in a 1(1/2)-year-old infant.

Key words: mastocytosis, classification, diagnosis, case report.

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For citation:Tamrazova O.B., Glukhova E.A. Cutaneous types of mastocytosis in paediatry. Case report of maculopapular cutaneous mastocytosis in an infant. Clinical review for general practice. 2020; 1: 60–66. DOI: 10.47407/kr2020.1.1.00009

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Clinical review for general practice