Clinical review for general practice

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ISSN (Online) 2782-5671
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FULLSCREEN > Archive > 2024 > Vol 5, №10 (2024) > Idiopathic lobular panniculitis. Clinical case

Idiopathic lobular panniculitis. Clinical case

Nikolay V. Ovsyannikov , Olga V. Zamakhina , Dmitrij R. Mingulov , Vladimir F. Gorshkov , Vitalij V. Klishin

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Abstract

Panniculitis includes heterogeneous diseases characterized by an immuno-inflammatory process in the subcutaneous fat. Often the musculoskeletal system and internal organs are involved in the pathological process. The etiology and pathogenesis of panniculitis are not fully understood, however, the immunopathological nature of the disease is most likely. There is no uniform classification of panniculitis. Ideopathic lobular panniculitis (ILP) (synonyms: recurrent febrile non-suppurating panniculitis, nodular Pfeiffer-Weber-Christian panniculitis) is of particular clinical interest. ILP according to ICD-10 refers to systemic connective tissue lesions (M 35.6). The described clinical case of IPD demonstrates the difficulty of diagnosing this disease.
Keywords: Pfeifer-Weber-Christian Disease, idiopathic nodular panniculitis, systemic connective tissue disease.

About the Author

Nikolay V. Ovsyannikov 1 , Olga V. Zamakhina 2 , Dmitrij R. Mingulov 2 , Vladimir F. Gorshkov 2 , Vitalij V. Klishin 2

1 Omsk State Medical University, Omsk, Russia

2 City Clinical Hospital No. 1 named after A.N. Kabanov, Omsk, Russia

References

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For citation:10.47407/kr2024.5.10.00492


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